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Dernières publications
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
59 %
Mots clés
Adipose tissue
CS
AAV
CD49d
Xenograft
Myosin
Regeneration
Metabolism
AAV vectors
Skeletal muscle
Cell therapy
Intercellular communication
Haploinsufficiency
Gene replacement
Satellite cells
Annexin A2
Gene therapy
Botulinum neurotoxin
Myopathies
Atrophy
Akt
Myositis
Duchenne muscular dystrophy
Myoblast
Dysferlinopathy
Satellite cell
Alphavirus
Lamins
Myogenesis
Pharyngeal muscle
2-D PAGE
DNA methylation
Nuclear envelope
BINDING SPECIFICITY
CNOT6L
Agrégats de PABPN1
Pax7
Autoimmune diseases
Arbovirus
Cross-bridge kinetics
Antiserum
DUX4
Biomarker
Aggregate
Myotube
Fibrosis
FAPs
Biopsies humaines
AUTOPHAGY
Dystrophin
Thérapie génique
Triplet expansion disease
PABPN1
Actin
Muscle
Neuromuscular junction NMJ
FSHD
MUTATIONS
Bioinformatics
AChR antibodies
Muscle stem cells
Oculopharyngeal muscular dystrophy
Alzheimer's disease
Inflammation
Transcriptomics
Ageing
Bile salt hydrolases
Anti-fibrotic pharmacotherapies
Exon-skipping
C2 domains
Bioinformatique
DMD
Aav-U7
Muscle dystrophy
Muscle strength
Myoblasts
Functional genomics
Human
Geriatric assessment
PABPN1 agregates
Myopathy
Muscle fibrosis
Aged
RNA
Accelerometry
C2C12 cells
Dystrophie musculaire oculopharyngée
GENE
Calcium
APOPTOSIS
ARN
Sarcopenia
Anti-acetylcholine receptor antibodies
Dysferlin
Autologous
ALS
Andermann syndrome
Antisens oligonucleotides
OPMD
Differentiation