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Dernières publications
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
59 %
Mots clés
Dysferlinopathy
Annexin A2
BINDING SPECIFICITY
Ageing
FAPs
Xenograft
Geriatric assessment
CS
MUTATIONS
Andermann syndrome
Myogenesis
GENE
AUTOPHAGY
Autoimmune diseases
Bioinformatics
Alphavirus
Differentiation
Aggregate
Accelerometry
Myoblast
APOPTOSIS
Anti-fibrotic pharmacotherapies
Satellite cell
Sarcopenia
Myotube
Pax7
Metabolism
Agrégats de PABPN1
Fibrosis
DNA methylation
Exon-skipping
Bile salt hydrolases
Muscle dystrophy
Functional genomics
2-D PAGE
Triplet expansion disease
Autologous
Pharyngeal muscle
Anti-acetylcholine receptor antibodies
Actin
AChR antibodies
Myositis
Bioinformatique
Lamins
Dystrophin
Adipose tissue
PABPN1
Thérapie génique
C2 domains
Cell therapy
Botulinum neurotoxin
RNA
Biomarker
Inflammation
Regeneration
Gene therapy
Human
PABPN1 agregates
Muscle fibrosis
DMD
Akt
Intercellular communication
Skeletal muscle
Muscle stem cells
Nuclear envelope
Alzheimer's disease
Antisens oligonucleotides
Myosin
DUX4
Gene replacement
Satellite cells
Antiserum
Calcium
CD49d
Aged
Muscle
C2C12 cells
ARN
Neuromuscular junction NMJ
Atrophy
Duchenne muscular dystrophy
OPMD
ALS
Transcriptomics
Myopathies
Myopathy
FSHD
Muscle strength
Dystrophie musculaire oculopharyngée
Biopsies humaines
Myoblasts
CNOT6L
Cross-bridge kinetics
AAV vectors
Dysferlin
AAV
Haploinsufficiency
Oculopharyngeal muscular dystrophy
Aav-U7
Arbovirus